Year : 2020

Volume : Volume 11

Issue : Issue 3

Address for correspondence :
Dr. Harsha Gorrela.
drgharshaomfs@gmail.com

Abstract

Background:  Goltz Gorlin syndrome is a rare autosomal disorder with strong penetrance and extremely variable expressivity that is often missed in diagnosis and treated for multiple odontogenic keratocysts. Early diagnosis of the syndrome is important due to susceptibility to carcinomas, and the syndrome can become destructive as age advances. Most often, the syndrome will be rarely diagnosed due to a lack of proper investigations. Here we present a case report of a patient with multiple odontogenic keratocysts diagnosed with Goltz Gorlin syndrome.

Keywords: Goltz Gorlin syndrome, multiple odontogenic keratocysts, Nbcc syndrome.